Cystic Fibrosis
"Cystic Fibrosis" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
An autosomal recessive genetic disease of the EXOCRINE GLANDS. It is caused by mutations in the gene encoding the CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR expressed in several organs including the LUNG, the PANCREAS, the BILIARY SYSTEM, and the SWEAT GLANDS. Cystic fibrosis is characterized by epithelial secretory dysfunction associated with ductal obstruction resulting in AIRWAY OBSTRUCTION; chronic RESPIRATORY INFECTIONS; PANCREATIC INSUFFICIENCY; maldigestion; salt depletion; and HEAT PROSTRATION.
Descriptor ID |
D003550
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MeSH Number(s) |
C06.689.202 C08.381.187 C16.320.190 C16.614.213
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Concept/Terms |
Pancreatic Cystic Fibrosis- Pancreatic Cystic Fibrosis
- Cystic Fibrosis, Pancreatic
- Fibrocystic Disease of Pancreas
- Pancreas Fibrocystic Disease
- Pancreas Fibrocystic Diseases
- Cystic Fibrosis of Pancreas
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Below are MeSH descriptors whose meaning is more general than "Cystic Fibrosis".
Below are MeSH descriptors whose meaning is more specific than "Cystic Fibrosis".
This graph shows the total number of publications written about "Cystic Fibrosis" by people in this website by year, and whether "Cystic Fibrosis" was a major or minor topic of these publications.
To see the data from this visualization as text, click here.
Year | Major Topic | Minor Topic | Total |
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1994 | 1 | 0 | 1 | 1995 | 1 | 0 | 1 | 2000 | 1 | 0 | 1 | 2004 | 1 | 1 | 2 | 2009 | 1 | 0 | 1 | 2014 | 1 | 0 | 1 | 2015 | 2 | 0 | 2 | 2019 | 1 | 0 | 1 |
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Below are the most recent publications written about "Cystic Fibrosis" by people in Profiles.
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Jorth P, Ehsan Z, Rezayat A, Caldwell E, Pope C, Brewington JJ, Goss CH, Benscoter D, Clancy JP, Singh PK. Direct Lung Sampling Indicates That Established Pathogens Dominate Early Infections in Children with Cystic Fibrosis. Cell Rep. 2019 04 23; 27(4):1190-1204.e3.
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Ehsan Z, Clancy JP. Management of Pseudomonas aeruginosa infection in cystic fibrosis patients using inhaled antibiotics with a focus on nebulized liposomal amikacin. Future Microbiol. 2015; 10(12):1901-12.
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Poppert KM, Patton SR, Borner KB, Davis AM, Dreyer Gillette ML. Systematic review: mealtime behavior measures used in pediatric chronic illness populations. J Pediatr Psychol. 2015 Jun; 40(5):475-86.
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Ehsan Z, Wetzel JD, Clancy JP. Nebulized liposomal amikacin for the treatment of Pseudomonas aeruginosa infection in cystic fibrosis patients. Expert Opin Investig Drugs. 2014 May; 23(5):743-9.
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Black PG, Derse AR, Derrington S, Lantos JD. Can a patient designate his doctor as his proxy decision maker? Pediatrics. 2013 May; 131(5):986-90.
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Taylor JB, Hogue LA, LiPuma JJ, Walter MJ, Brody SL, Cannon CL. Entry of Burkholderia organisms into respiratory epithelium: CFTR, microfilament and microtubule dependence. J Cyst Fibros. 2010 Jan; 9(1):36-43.
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Copeland DR, St Peter SD, Sharp SW, Islam S, Cuenca A, Tolleson JS, Dassinger MS, Little DC, Jackson RJ, Kokoska ER, Smith SD. Diminishing role of contrast enema in simple meconium ileus. J Pediatr Surg. 2009 Nov; 44(11):2130-2.
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Kennedy MJ, Abdel-Rahman SM, Kashuba AD, Leeder JS. Comparison of various urine collection intervals for caffeine and dextromethorphan phenotyping in children. J Clin Pharmacol. 2004 Jul; 44(7):708-14.
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Kennedy MJ, Scripture CD, Kashuba AD, Scott CS, Gaedigk A, Kearns GL. Activities of cytochrome P450 1A2, N-acetyltransferase 2, xanthine oxidase, and cytochrome P450 2D6 are unaltered in children with cystic fibrosis. Clin Pharmacol Ther. 2004 Mar; 75(3):163-71.
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Attard TM, Askin FB, Cuffari C. Appendiceal inversion as a lead point for ileocolic intussusception in a child with cystic fibrosis. J Pediatr Gastroenterol Nutr. 2000 Sep; 31(3):300-2.
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